Imanov E., Dzyurii I., Pliska O., Truba Y., Lazoryshynets V.


About the author:

Imanov E., Dzyurii I., Pliska O., Truba Y., Lazoryshynets V.



Type of article:

Scentific article


Total anomalous pulmonary venous connection (TAPVC) is a rare cyanotic congenital heart defect that occurs from 1% to 3% of all congenital heart abnormalities. Without cardiac surgery, most patients (about 80%) with TAPVC die within the first year of life. The treatment of such patients is a complex and difficult problem. Up to now, surgical correction of this defect is accompanied by a significant mortality rate. The aim of this work is to analyze the results of surgical treatment of total anomalous pulmonary venous connection in children operated from 2006 to 2018. Object and methods. For the period from 2006 to 2018 at the “National Amosov Institute of Cardiovascular Surgery” treated 34 consecutive patients with TAPVC. The mean age of the patients was 109.3±101.4 days (from 2 to 505 days), respectively, and mean weight was 4.01±1.1 kg. It was found that in 57.1% (20) patients there was a supracardiac form of anomaly, in 14.2% (5) – an intracardiac form, in 17.1% (6) of patients – infracardiac and in 11.4% (4) – mixed form. Results. Two patients (5.8%) died in the postoperative period. The causes of death among patients were: progressive heart failure (n = 1), which was a consequence of small size of the left ventricle, one patient died after pulmonary hypertensive crises due to increased reactivity of the pulmonary vessels in the early postoperative period. Conclusion. Total anomalous pulmonary venous connection belongs to the group of complex congenital heart defects. In recent years, due to the development of prenatal and improving the quality of postnatal diagnosis, changes in treatment tactics, improvement of surgical techniques, the level of postoperative mortality has decreased significantly.


congenital heart defect, total anomalous pulmonary venous connection, infants.


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Publication of the article:

«Bulletin of problems biology and medicine» Issue 4 Part 2 (154), 2019 year, 91-94 pages, index UDK 616.12-007.2-053.2:616.141]-089.168